Congenital: Aortic Valve
- Ring annuloplasty has been used routinely for surgical repair of tricuspid and mitral valves for more than 35 years, and more recently, a similar ring has been developed for bicuspid aortic valve (BAV) repair.1 Annuloplasty rings restore normal size and geometry of the valve annulus, bring the native leaflets into better coaptation, and prevent future annular dilatation. In this article, the first case of a pediatric patient with a BAV and severe aortic insufficiency (AI) managed with internal ring annuloplasty is presented.
- The Bentall procedure1 is rarely performed in pediatric patients, with exceptions such as connective tissue disorder. We report a young adult patient presenting prosthesis–patient mismatch after the Bentall procedure.
- Midaortic syndrome (MAS) is narrowing of the descending thoracoabdominal aorta. Symptomatic MAS is associated with high mortality in neonates and infants.1 We describe the case of a 4-month-old infant with MAS and illustrate a staged, multidisciplinary, and multimodality approach.
- Coarctation of aorta aneurysm with aberrant right subclavian artery and single carotid artery is a rare and complex congenital aortic anomaly. We present the surgical and perfusion strategy that we used to maintain cerebral and spinal cord perfusion during repair, thereby preventing devastating complications of stroke and paraplegia. Written patient consent was obtained for this case report.
- Use of percutaneous pulmonary valve replacement (PPVR) has steadily increased during the last decade, even though increased risk of endocarditis continues to be a concern.1,2 The close proximity of the right ventricle–pulmonary artery (RV-PA) conduit to the dilated neoaorta after the Ross operation poses unique challenges for PPVR. Stent fractures, accelerated progression of neoaortic regurgitation, aortopulmonary fistula, and coronary compression are well-documented complications of PPRV after the Ross operation.