In patients with hypoplastic left heart syndrome (HLHS) and right ventricular (RV) dilatation and failure, tricuspid valve (TV) replacement is rarely performed after Fontan completion.1 Listing for heart transplantation, or considering long-term mechanical circulatory support as a bridge to transplantation, is the conventional approach.2 We describe a patient with HLHS and failing Fontan circulation, with severe RV dilatation and severe TV regurgitation. The patient was not a candidate for heart transplantation.
In patients with hypoplastic left heart syndrome (HLHS) and right ventricular (RV) dilatation and failure, tricuspid valve (TV) replacement is rarely performed after Fontan completion.1 Listing for heart transplantation, or considering long-term mechanical circulatory support as a bridge to transplantation, is the conventional approach.2 We describe a patient with HLHS and failing Fontan circulation, with severe RV dilatation and severe TV regurgitation. The patient was not a candidate for heart transplantation.