
Petros V. Anagnostopoulos, MD
Central Message
A well-rounded training program that exposes trainees to a breadth of experience may come in handy when coming across a lesion that requires an unusual repair.
See Article page e341.
Quadricuspid aortic valves (QAVs) are very rare but have been well described since the early 1970s.
1
Even less recognized but documented is the association of QAVs with a potential congenital structural aortopathy. In the largest series of QAVs to date, 42% of patients had ascending aortic diameters greater than or equal to 4 cm.2
Most patients with QAVs present with aortic insufficiency, aortic stenosis, or a combination of these. In this issue of the Journal, Xu and associates3
report on a 35-year-old woman who presented with a QAV associated with a ruptured sinus of Valsalva aneurysm. A tricuspidization procedure was performed, with resection of the smaller ruptured right anterior sinus of Valsalva with the associated cusp, with a great clinical outcome. Time will tell whether this will lead to a durable long-term result. Although the technique of tricuspidization is well described in QAVs, it was first applied in truncus arteriosus repair.4
Information regarding the long-term outcomes after these repairs in truncus arteriosus exists in the congenital literature.5
This interesting report underscores the importance of well-rounded surgical training and education, with exposure to complex repair techniques of different acquired and congenital heart pathologies. One simply never knows when the patient will show up who is a great candidate for an unusual repair technique that uses principles that have been described in a totally different setting. This becomes ever more important as trainees are asked to master new technologies or to focus on a niche in adult cardiac surgery to remain competitive in the marketplace. Such subspecialty focus typically occurs at the expense of hands-on time and exposure to congenital heart surgery.
References
- Quadricuspid semilunar valve.Am J Cardiol. 1973; 31: 623-626
- Outcomes after repair or replacement of dysfunctional quadricuspid aortic valve.J Thorac Cardiovasc Surg. 2015; 150: 79-82
- Surgical repair of quadricuspid aortic valve associated with ruptured sinus of Valsalva aneurysm.J Thorac Cardiovasc Surg. 2020; 159: e341-e342
- Improving early and intermediate results of truncus arteriosus repair: a new technique of truncal valve repair.Ann Thorac Surg. 1999; 67: 1142-1146
- Surgical repair of truncal valve regurgitation.Eur J Cardiothorac Surg. 2013; 44: 813-820
Article info
Publication history
Published online: July 25, 2019
Accepted:
July 17,
2019
Received:
July 16,
2019
Footnotes
Disclosures: Author has nothing to disclose with regard to commercial support.
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© 2019 by The American Association for Thoracic Surgery
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- Surgical repair of a quadricuspid aortic valve associated with a ruptured sinus of Valsalva aneurysmThe Journal of Thoracic and Cardiovascular SurgeryVol. 159Issue 6
- PreviewA 35-year-old woman presented with a history of gradually worsening dyspnea on exertion. Clinical examination revealed a diastolic murmur heard loudest along the upper left sternal border, which did not radiate to the carotids or the precordium. Transthoracic echocardiography demonstrated a quadricuspid aortic valve (type A, Hurwitz and Robert's classification) with an aorta-to-right atrium fistula (sinus 2) through a ruptured right-anterior sinus of Valsalva (Figure 1, A). In addition, the coronary orifices originated from sinus 1 (right coronary artery) and sinus 4 (left main coronary artery), and the aortic regurgitation was moderate (Figure 1, A and B).
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